Far from rare: revisiting the relevance of idiopathic basal ganglia calcifications

fahr disease: idiopathic basal ganglia calcification

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Transcranial sonography of basal ganglia calcifications in Fahr disease.

Fahr disease, also known as bilateral striopallidodentate calcinosis, is a rare degenerative neurologic disorder characterized by almost symmetric calcifications of the basal ganglia, the cerebellum dentate nuclei, the thalami, and the white matter of the cerebral hemispheres. Bilateral striopallidodentate calcinosis manifests as familial autosomal dominant but also as sporadic forms. Movement ...

Bilateral basal ganglia calcifications visualised on CT scan.

Thirty-eight cases of basal ganglia calcification imaged on computed axial tomography were reviewed. Most cases were felt to represent senescent calcification. The possibility of a vascular aetiology in this group is discussed. A less common group of patients was identified with calcification secondary to abnormalities in calcium metabolism or radiation therapy. Three cases of basal ganglia cal...

Fahr disease: Idiopathic basal ganglia calcification

Familial idiopathic basal ganglia calcification (Fahr’s disease)

Familial idiopathic basal ganglia calcification (Fahr`s disease) is a rare neurodegenerative disorder characterized by symmetrical and bilateral calcification of the basal ganglia. Calcifications may also occur in other brain regions such as dentate nucleus, thalamus, and cerebral cortex. Both familial and non-familial cases of Fahr`s disease have been reported, predominantly with autosomal-dom...